AIPL1 purified MaxPab rabbit polyclonal antibody (D01P)
产品名称： AIPL1 purified MaxPab rabbit polyclonal antibody (D01P)
英文名称： AIPL1 purified MaxPab rabbit polyclonal antibody (D01P)
产品编号： H00023746-D01P
产品价格： null
产品产地： 台湾
品牌商标： Abnova
更新时间： null
使用范围：
亚诺法生技股份有限公司（Abnova)
- 联系人 :
- 地址 : 台湾台北市内湖区洲子街 108 号 9 楼
- 邮编 : 11493
- 所在区域 : 台湾
- 电话 : +886-920**1152 点击查看
- 传真 : 点击查看
- 邮箱 : sales@abnova.com.tw
- Specification
- Product Description:
- Rabbit polyclonal antibody raised against a full-length human AIPL1 protein.
- Immunogen:
- AIPL1 (NP_055151.3, 1 a.a. ~ 384 a.a) full-length human protein.
- Sequence:
- MDAALLLNVEGVKKTILHGGTGELPNFITGSRVIFHFRTMKCDEERTVIDDSRQVGQPMHIIIGNMFKLEVWEILLTSMRVHEVAEFWCDTIHTGVYPILSRSLRQMAQGKDPTEWHVHTCGLANMFAYHTLGYEDLDELQKEPQPLVFVIELLQVDAPSDYQRETWNLSNHEKMKAVPVLHGEGNRLFKLGRYEEASSKYQEAIICLRNLQTKEKPWEVQWLKLEKMINTLILNYCQCLLKKEEYYEVLEHTSDILRHHPGIVKAYYVRARAHAEVWNEAEAKADLQKVLELEPSMQKAVRRELRLLENRMAEKQEEERLRCRNMLSQGATQPPAEPPTEPPAQSSTEPPAEPPTAPSAELSAGPPAEPATEPPPSPGHSLQH
- Host:
- Rabbit
- Reactivity:
- Human
- Storage Buffer:
- In 1x PBS, pH 7.2
- Storage Instruction:
- Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
- Quality Control Testing:
- Antibody reactive against mammalian transfected lysate.
- MSDS:
Download
- Applications
- Western Blot (Transfected lysate)
- Western Blot analysis of AIPL1 expression in transfected 293T cell line (H00023746-T01) by AIPL1 MaxPab polyclonal antibody.
Lane 1: AIPL1 transfected lysate(43.90 KDa).
Lane 2: Non-transfected lysate. - Protocol Download
- Entrez GeneID:
- 23746
- GeneBank Accession#:
- NM_014336.3
- Protein Accession#:
- NP_055151.3
- Gene Name:
- AIPL1
- Gene Alias:
- AIPL2,LCA4
- Gene Description:
- aryl hydrocarbon receptor interacting protein-like 1
- Gene Ontology:
- Hyperlink
- Gene Summary:
- Leber congenital amaurosis (LCA) accounts for at least 5% of all inherited retinal disease and is the most severe inherited retinopathy with the earliest age of onset. Individuals affected with LCA are diagnosed at birth or in the first few months of life with severely impaired vision or blindness, nystagmus and an abnormal or flat electroretinogram. The photoreceptor/pineal -expressed gene, AIPL1, encoding aryl-hydrocarbon interacting protein-like 1, was mapped within the LCA4 candidate region. The protein contains three tetratricopeptide motifs, consistent with nuclear transport or chaperone activity. AIPL1 mutations may cause approximately 20% of recessive LCA. [provided by RefSeq
- Other Designations:
- -